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Abnormal prion protein in the pituitary in sporadic and variant Creutzfeldt-Jakob disease

artículo científico publicado en 2007

Advances in the development of a screening test for variant Creutzfeldt–Jakob disease

scientific article published on 01 February 2008

Detection and localization of PrPSc in the skeletal muscle of patients with variant, iatrogenic, and sporadic forms of Creutzfeldt-Jakob disease

artículo científico publicado en 2006

Distinct stability states of disease-associated human prion protein identified by conformation-dependent immunoassay

artículo científico publicado en 2010

Effects of human PrPSc type and PRNP genotype in an in-vitro conversion assay

artículo científico publicado en 2008

Epitope mapping of the protease resistant products of RT-QuIC does not allow the discrimination of sCJD subtypes

scientific article published on 17 June 2019

Human platelets as a substrate source for the in vitro amplification of the abnormal prion protein (PrP) associated with variant Creutzfeldt-Jakob disease

artículo científico publicado en 2008

Preclinical vCJD after blood transfusion in a PRNP codon 129 heterozygous patient

artículo científico publicado en 2004

Sensitive and specific detection of sporadic Creutzfeldt-Jakob disease brain prion protein using real-time quaking-induced conversion

artículo científico publicado en 2011

Stimulation of p70S6 kinase via a growth hormone-controlled phosphatidylinositol 3-kinase pathway leads to the activation of a PDE4A cyclic AMP-specific phosphodiesterase in 3T3-F442A preadipocytes

artículo científico publicado el 31 de marzo de 1998

Study protocol for enhanced CJD surveillance in the 65+ years population group in Scotland: an observational neuropathological screening study of banked brain tissue donations for evidence of prion disease

artículo científico publicado en 2019

The application of in vitro cell-free conversion systems to human prion diseases

artículo científico publicado en 2010

The prion protein protease sensitivity, stability and seeding activity in variably protease sensitive prionopathy brain tissue suggests molecular overlaps with sporadic Creutzfeldt-Jakob disease

artículo científico publicado en 2014

Variably protease-sensitive prionopathy, a unique prion variant with inefficient transmission properties

artículo científico publicado en 2014