Lista de obras -

A Novel Pkhd1 Mutation Interacts with the Nonobese Diabetic Genetic Background To Cause Autoimmune Cholangitis

artículo científico publicado en 2017

A Phase I/IIa Trial of Intravenous Immunoglobulin Following Portoenterostomy in Biliary Atresia

artículo científico publicado en 2019

A multicenter study of the outcome of biliary atresia in the United States, 1997 to 2000

artículo científico publicado en 2006

Advances in biliary atresia: from patient care to research

artículo científico publicado en 2010

Analysis of gene mutations in children with cholestasis of undefined etiology

artículo científico publicado en 2010

Analysis of the biliary transcriptome in experimental biliary atresia

artículo científico publicado en 2005

BILIARY ATRESIA: Clinical and Research Challenges for the 21st Century.

artículo científico publicado en 2018

Biliary atresia and Th1 function: linking lymphocytes and bile ducts: commentary on the article by Mack et al. on page 79.

artículo científico publicado en 2004

Biliary atresia and other cholestatic childhood diseases: Advances and future challenges.

artículo científico publicado en 2016

Biliary atresia: will blocking inflammation tame the disease?

artículo científico publicado en 2011

Biliary repair and carcinogenesis are mediated by IL-33-dependent cholangiocyte proliferation

artículo científico publicado en 2014

Cholestasis: current issues and plan for the future.

artículo científico publicado en 2008

Congenital Portosystemic Shunts in Children: Associations, Complications, and Outcomes

artículo científico publicado en 2019

Coordinate expression of regulatory genes differentiates embryonic and perinatal forms of biliary atresia

artículo científico publicado en 2004

Correlation of Immune Markers With Outcomes in Biliary Atresia Following Intravenous Immunoglobulin Therapy

Cxcr2 signaling and the microbiome suppress inflammation, bile duct injury, and the phenotype of experimental biliary atresia

artículo científico publicado en 2017

Dendritic Cells Regulate Natural Killer Cell Activation and Epithelial Injury in Experimental Biliary Atresia ⬇️

artículo científico publicado el 28 de septiembre de 2011

Diagnostic Accuracy of Serum Matrix Metalloproteinase-7 for Biliary Atresia

scientific article published on 15 November 2018

Effect of rotavirus strain on the murine model of biliary atresia

artículo científico publicado en 2006

Effector role of neonatal hepatic CD8+ lymphocytes in epithelial injury and autoimmunity in experimental biliary atresia

artículo científico publicado en 2007

Efficacy of Fat-Soluble Vitamin Supplementation in Infants With Biliary Atresia ⬇️

artículo científico publicado el 13 de agosto de 2012

Extrahepatic Anomalies in Infants With Biliary Atresia: Results of a Large Prospective North American Multicenter Study ⬇️

artículo científico publicado el 19 de septiembre de 2013

Gene Expression Signatures Associated With Survival Times of Pediatric Patients With Biliary Atresia Identify Potential Therapeutic Agents

scientific article published on 19 June 2019

Gene expression signature for biliary atresia and a role for interleukin-8 in pathogenesis of experimental disease

artículo científico publicado en 2014

Gene-disease associations identify a connectome with shared molecular pathways in human cholangiopathies

artículo científico

Genetic induction of proinflammatory immunity in children with biliary atresia

artículo científico publicado en 2002

Genetic modifiers of cholestatic liver disease: an evolving field

scientific article published on 01 January 2006

Growth failure and outcomes in infants with biliary atresia: a report from the Biliary Atresia Research Consortium

artículo científico publicado en 2007

Hepatic to pancreatic switch defines a role for hemostatic factors in cellular plasticity in mice

artículo científico publicado en 2005

High prevalence of alpha-1-antitrypsin heterozygosity in children with chronic liver disease

artículo científico publicado en 2007

IL-33 facilitates oncogene-induced cholangiocarcinoma in mice by an interleukin-6-sensitive mechanism

artículo científico publicado en 2015

Identification of Polycystic Kidney Disease 1 Like 1 Gene Variants in Children With Biliary Atresia Splenic Malformation Syndrome

artículo científico publicado en 2019

Identification of intramural epithelial networks linked to peribiliary glands that express progenitor cell markers and proliferate after injury in mice ⬇️

artículo científico publicado el 6 de agosto de 2013

Impact of Steroid Therapy on Early Growth in Infants with Biliary Atresia: The Multicenter Steroids in Biliary Atresia Randomized Trial

artículo científico publicado en 2018

Increased frequency of double and triple heterozygous gene variants in children with intrahepatic cholestasis

artículo científico publicado en 2015

Independent and overlapping transcriptional activation during liver development and regeneration in mice

scientific article published on 01 March 2002

Initial assessment of the infant with neonatal cholestasis-Is this biliary atresia?

artículo científico publicado en 2017

Integrative genomics identifies candidate microRNAs for pathogenesis of experimental biliary atresia

artículo científico publicado en 2013

Intrahepatic cholestasis: summary of an American Association for the Study of Liver Diseases single-topic conference

artículo científico publicado en 2005

Lampe1: an ENU-germline mutation causing spontaneous hepatosteatosis identified through targeted exon-enrichment and next-generation sequencing.

artículo científico publicado en 2011

Large-scale proteomics identifies MMP-7 as a sentinel of epithelial injury and of biliary atresia.

artículo científico publicado en 2017

Liver transplantation in children younger than 1 year--the Cincinnati experience.

artículo científico publicado en 2005

Loss of interleukin-12 modifies the pro-inflammatory response but does not prevent duct obstruction in experimental biliary atresia

artículo científico publicado en 2006

Macrophages are targeted by rotavirus in experimental biliary atresia and induce neutrophil chemotaxis by Mip2/Cxcl2.

artículo científico publicado en 2010

Modeling Outcomes in Children With Biliary Atresia With Native Liver After 2 Years of Age

artículo científico publicado en 2020

Natural Course of Pediatric Portal Hypertension

scientific article published on 16 July 2020

Natural killer cells promote long-term hepatobiliary inflammation in a low-dose rotavirus model of experimental biliary atresia

artículo científico publicado en 2015

Neonatal NK cells target the mouse duct epithelium via Nkg2d and drive tissue-specific injury in experimental biliary atresia

artículo científico publicado en 2009

Neurodevelopmental Outcome of Young Children with Biliary Atresia and Native Liver: Results from the ChiLDReN Study

artículo científico publicado en 2018

Neurodevelopmental Outcomes in Preschool and School Aged Children With Biliary Atresia and Their Native Liver

artículo científico publicado en 2020

Nonfasted Liver Stiffness Correlates with Liver Disease Parameters and Portal Hypertension in Pediatric Cholestatic Liver Disease

artículo científico publicado en 2020

Novel genes and functional relationships in the adult mouse gastrointestinal tract identified by microarray analysis

artículo científico publicado en 2002

Novel resequencing chip customized to diagnose mutations in patients with inherited syndromes of intrahepatic cholestasis

artículo científico

Obstruction of extrahepatic bile ducts by lymphocytes is regulated by IFN-gamma in experimental biliary atresia

artículo científico publicado en 2004

Paracrine signals regulate human liver organoid maturation from induced pluripotent stem cells

artículo científico publicado en 2017

Pathogenesis of biliary atresia: defining biology to understand clinical phenotypes

artículo científico publicado en 2015

Perforin and granzymes work in synergy to mediate cholangiocyte injury in experimental biliary atresia

artículo científico publicado en 2013

Plasmin-mediated proteolysis is required for hepatocyte growth factor activation during liver repair

artículo científico publicado en 2009

Plasminogen directs the pleiotropic effects of uPA in liver injury and repair

artículo científico publicado en 2002

Preferential TNFα signaling via TNFR2 regulates epithelial injury and duct obstruction in experimental biliary atresia

artículo científico publicado en 2017

Prospective Assessment of Ultrasound Shear Wave Elastography for Discriminating Biliary Atresia from other Causes of Neonatal Cholestasis

scientific article published on 26 June 2019

Regulation of epithelial injury and bile duct obstruction by NLRP3, IL-1R1 in experimental biliary atresia

artículo científico publicado en 2018

Replication of a GWAS signal in a Caucasian population implicates ADD3 in susceptibility to biliary atresia

artículo científico publicado en 2013

Reply: To PMID 24493287

artículo científico publicado en 2014

Screening and outcomes in biliary atresia: summary of a National Institutes of Health workshop.

artículo científico publicado en 2007

Single cell RNA sequencing reveals regional heterogeneity of hepatobiliary innate lymphoid cells in a tissue-enriched fashion

scientific article published on 25 April 2019

Staging of biliary atresia at diagnosis by molecular profiling of the liver

artículo científico publicado en 2010

Temporal-spatial activation of apoptosis and epithelial injury in murine experimental biliary atresia

artículo científico publicado en 2008

Th2 signals induce epithelial injury in mice and are compatible with the biliary atresia phenotype

artículo científico publicado en 2011

The beneficial impact of revision of Kasai portoenterostomy for biliary atresia: an institutional study

artículo científico

Total Serum Bilirubin within 3 Months of Hepatoportoenterostomy Predicts Short-Term Outcomes in Biliary Atresia

artículo científico publicado en 2015

Total serum bilirubin predicts fat-soluble vitamin deficiency better than serum bile acids in infants with biliary atresia

artículo científico publicado en 2014

Transcriptional reprogramming in murine liver defines the physiologic consequences of biliary obstruction

artículo científico publicado en 2004

Urokinase-type plasminogen activator supports liver repair independent of its cellular receptor

artículo científico publicado en 2006

Use of corticosteroids after hepatoportoenterostomy for bile drainage in infants with biliary atresia: the START randomized clinical trial

artículo científico publicado en 2014

Lista de obras de

A Novel Pkhd1 Mutation Interacts with the Nonobese Diabetic Genetic Background To Cause Autoimmune Cholangitis

A Phase I/IIa Trial of Intravenous Immunoglobulin Following Portoenterostomy in Biliary Atresia

A multicenter study of the outcome of biliary atresia in the United States, 1997 to 2000

Advances in biliary atresia: from patient care to research

Analysis of gene mutations in children with cholestasis of undefined etiology

Analysis of the biliary transcriptome in experimental biliary atresia

BILIARY ATRESIA: Clinical and Research Challenges for the 21st Century.

Biliary atresia and Th1 function: linking lymphocytes and bile ducts: commentary on the article by Mack et al. on page 79.

Biliary atresia and other cholestatic childhood diseases: Advances and future challenges.

Biliary atresia: will blocking inflammation tame the disease?

Biliary repair and carcinogenesis are mediated by IL-33-dependent cholangiocyte proliferation

Cholestasis: current issues and plan for the future.

Congenital Portosystemic Shunts in Children: Associations, Complications, and Outcomes

Coordinate expression of regulatory genes differentiates embryonic and perinatal forms of biliary atresia

Correlation of Immune Markers With Outcomes in Biliary Atresia Following Intravenous Immunoglobulin Therapy

Cxcr2 signaling and the microbiome suppress inflammation, bile duct injury, and the phenotype of experimental biliary atresia

Dendritic Cells Regulate Natural Killer Cell Activation and Epithelial Injury in Experimental Biliary Atresia ⬇️

Diagnostic Accuracy of Serum Matrix Metalloproteinase-7 for Biliary Atresia

Effect of rotavirus strain on the murine model of biliary atresia

Effector role of neonatal hepatic CD8+ lymphocytes in epithelial injury and autoimmunity in experimental biliary atresia

Efficacy of Fat-Soluble Vitamin Supplementation in Infants With Biliary Atresia ⬇️

Extrahepatic Anomalies in Infants With Biliary Atresia: Results of a Large Prospective North American Multicenter Study ⬇️

Gene Expression Signatures Associated With Survival Times of Pediatric Patients With Biliary Atresia Identify Potential Therapeutic Agents

Gene expression signature for biliary atresia and a role for interleukin-8 in pathogenesis of experimental disease

Gene-disease associations identify a connectome with shared molecular pathways in human cholangiopathies

Genetic induction of proinflammatory immunity in children with biliary atresia

Genetic modifiers of cholestatic liver disease: an evolving field

Growth failure and outcomes in infants with biliary atresia: a report from the Biliary Atresia Research Consortium

Hepatic to pancreatic switch defines a role for hemostatic factors in cellular plasticity in mice

High prevalence of alpha-1-antitrypsin heterozygosity in children with chronic liver disease

IL-33 facilitates oncogene-induced cholangiocarcinoma in mice by an interleukin-6-sensitive mechanism

Identification of Polycystic Kidney Disease 1 Like 1 Gene Variants in Children With Biliary Atresia Splenic Malformation Syndrome

Identification of intramural epithelial networks linked to peribiliary glands that express progenitor cell markers and proliferate after injury in mice ⬇️

Impact of Steroid Therapy on Early Growth in Infants with Biliary Atresia: The Multicenter Steroids in Biliary Atresia Randomized Trial

Increased frequency of double and triple heterozygous gene variants in children with intrahepatic cholestasis

Independent and overlapping transcriptional activation during liver development and regeneration in mice

Initial assessment of the infant with neonatal cholestasis-Is this biliary atresia?

Integrative genomics identifies candidate microRNAs for pathogenesis of experimental biliary atresia

Intrahepatic cholestasis: summary of an American Association for the Study of Liver Diseases single-topic conference

Lampe1: an ENU-germline mutation causing spontaneous hepatosteatosis identified through targeted exon-enrichment and next-generation sequencing.

Large-scale proteomics identifies MMP-7 as a sentinel of epithelial injury and of biliary atresia.

Liver transplantation in children younger than 1 year--the Cincinnati experience.

Loss of interleukin-12 modifies the pro-inflammatory response but does not prevent duct obstruction in experimental biliary atresia

Macrophages are targeted by rotavirus in experimental biliary atresia and induce neutrophil chemotaxis by Mip2/Cxcl2.

Modeling Outcomes in Children With Biliary Atresia With Native Liver After 2 Years of Age

Natural Course of Pediatric Portal Hypertension

Natural killer cells promote long-term hepatobiliary inflammation in a low-dose rotavirus model of experimental biliary atresia

Neonatal NK cells target the mouse duct epithelium via Nkg2d and drive tissue-specific injury in experimental biliary atresia

Neurodevelopmental Outcome of Young Children with Biliary Atresia and Native Liver: Results from the ChiLDReN Study

Neurodevelopmental Outcomes in Preschool and School Aged Children With Biliary Atresia and Their Native Liver

Nonfasted Liver Stiffness Correlates with Liver Disease Parameters and Portal Hypertension in Pediatric Cholestatic Liver Disease

Novel genes and functional relationships in the adult mouse gastrointestinal tract identified by microarray analysis

Novel resequencing chip customized to diagnose mutations in patients with inherited syndromes of intrahepatic cholestasis

Obstruction of extrahepatic bile ducts by lymphocytes is regulated by IFN-gamma in experimental biliary atresia

Paracrine signals regulate human liver organoid maturation from induced pluripotent stem cells

Pathogenesis of biliary atresia: defining biology to understand clinical phenotypes

Perforin and granzymes work in synergy to mediate cholangiocyte injury in experimental biliary atresia

Plasmin-mediated proteolysis is required for hepatocyte growth factor activation during liver repair

Plasminogen directs the pleiotropic effects of uPA in liver injury and repair

Preferential TNFα signaling via TNFR2 regulates epithelial injury and duct obstruction in experimental biliary atresia

Prospective Assessment of Ultrasound Shear Wave Elastography for Discriminating Biliary Atresia from other Causes of Neonatal Cholestasis

Regulation of epithelial injury and bile duct obstruction by NLRP3, IL-1R1 in experimental biliary atresia

Replication of a GWAS signal in a Caucasian population implicates ADD3 in susceptibility to biliary atresia

Reply: To PMID 24493287

Screening and outcomes in biliary atresia: summary of a National Institutes of Health workshop.

Single cell RNA sequencing reveals regional heterogeneity of hepatobiliary innate lymphoid cells in a tissue-enriched fashion

Staging of biliary atresia at diagnosis by molecular profiling of the liver

Temporal-spatial activation of apoptosis and epithelial injury in murine experimental biliary atresia

Th2 signals induce epithelial injury in mice and are compatible with the biliary atresia phenotype

The beneficial impact of revision of Kasai portoenterostomy for biliary atresia: an institutional study

Total Serum Bilirubin within 3 Months of Hepatoportoenterostomy Predicts Short-Term Outcomes in Biliary Atresia

Total serum bilirubin predicts fat-soluble vitamin deficiency better than serum bile acids in infants with biliary atresia

Transcriptional reprogramming in murine liver defines the physiologic consequences of biliary obstruction

Urokinase-type plasminogen activator supports liver repair independent of its cellular receptor

Use of corticosteroids after hepatoportoenterostomy for bile drainage in infants with biliary atresia: the START randomized clinical trial