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A mast cell-ILC2-Th9 pathway promotes lung inflammation in cystic fibrosis

scientific article published on 16 January 2017

Amikacin containing self-emulsifying delivery systems via pulmonary administration for treatment of bacterial infections of cystic fibrosis patients

artículo científico publicado en 2018

Calculation of the capnographic index based on expiratory molar mass–volume-curves — A suitable tool to screen for cystic fibrosis lung disease

artículo científico publicado el 12 de septiembre de 2012

Cystic fibrosis (CF) care through the patients' eyes - a nationwide survey on experience and satisfaction with services using a disease-specific questionnaire.

artículo científico publicado en 2014

Cystic fibrosis in Austria

artículo científico publicado en 2017

Different approaches to evaluate patient experience and satisfaction in CF centres

artículo científico publicado en 2015

Evaluating patient experience in a cystic fibrosis centre using a disease-specific patient satisfaction questionnaire.

artículo científico publicado en 2015

Evidence for genetic heterogeneity in lymphedema-cholestasis syndrome

artículo científico publicado en 2003

Factors Associated with Worse Lung Function in Cystic Fibrosis Patients with Persistent Staphylococcus aureus

artículo científico publicado en 2016

Factors associated with FEV1 decline in cystic fibrosis: analysis of the ECFS patient registry.

artículo científico publicado en 2013

Faecal calprotectin concentrations in young children with cystic fibrosis

artículo científico publicado en 2017

Feasibility and Variability of Measuring the Lung Clearance Index in a Multi‐Center Setting

artículo científico publicado el 13 de diciembre de 2011

Fecal Calprotectin in Cystic Fibrosis and Its Relation to Disease Parameters: A Longitudinal Analysis for 12 Years

artículo científico publicado en 2017

Guidelines for the diagnosis and management of distal intestinal obstruction syndrome in cystic fibrosis patients

artículo científico publicado en 2011

Hygienic safety of an ultrasonic flow sensor for multiple breath washout

artículo científico publicado en 2009

IL-1 receptor antagonist ameliorates inflammasome-dependent inflammation in murine and human cystic fibrosis

artículo científico publicado en 2016

Immunohistochemical analysis of Mallory bodies in Wilsonian and non-Wilsonian hepatic copper toxicosis

artículo científico publicado en 2004

International prospective study of distal intestinal obstruction syndrome in cystic fibrosis: Associated factors and outcome.

artículo científico publicado en 2016

Long-term glomerular filtration rate following pediatric liver transplantation

artículo científico publicado en 2005

Long-term improvement of lung clearance index in patients with mild cystic fibrosis lung disease: Does hypertonic saline play a role?

artículo científico publicado en 2015

Low sodium status in cystic fibrosis-as assessed by calculating fractional Na(+) excretion-is associated with decreased growth parameters

artículo científico publicado en 2016

Lung clearance index to detect the efficacy of Aztreonam lysine inhalation in patients with cystic fibrosis and near normal spirometry - A single-centre feasibility study

scientific article published on 09 September 2019

Lung clearance index: normal values, repeatability, and reproducibility in healthy children and adolescents

artículo científico publicado en 2009

Patient experience in cystic fibrosis care: Development of a disease-specific questionnaire

artículo científico

Psychological resilience and intolerance of uncertainty in coping with cystic fibrosis.

artículo científico publicado en 2015

Sensitivity of Lung Clearance Index and chest computed tomography in early CF lung disease

artículo científico publicado en 2010

Severe cold agglutinin disease caused by recurrent monomorphic Epstein-Barr virus (EBV)-associated post-transplant lymphoproliferative disorder (PTLD), clonally related to an EBV-negative plasmacytic hyperplasia in a pediatric multivisceral organ tr

artículo científico publicado en 2007

Spectrum of imaging findings after intestinal, liver-intestinal, or multivisceral transplantation: part 1, posttransplantation anatomy

scientific article published on 01 November 2004

Spectrum of imaging findings after intestinal, liver-intestinal, or multivisceral transplantation: part 2, posttransplantation complications

scientific article published on 01 November 2004

Spectrum of imaging findings after pediatric liver transplantation: part 1, posttransplantation anatomy

artículo científico publicado en 2003

Spectrum of imaging findings after pediatric liver transplantation: part 2, posttransplantation complications

artículo científico publicado en 2003

The canine copper toxicosis gene MURR1 does not cause non-Wilsonian hepatic copper toxicosis

artículo científico publicado en 2003

Tracking Lung Clearance Index and chest CT in mild cystic fibrosis lung disease over a period of three years

artículo científico publicado en 2014