Lista de obras - Simon R. Johnson - Dominio Público Uruguay

A 2-year randomised placebo-controlled trial of doxycycline for lymphangioleiomyomatosis.

artículo científico publicado en 2013

A 4-year prospective evaluation of protocols to improve clinical outcomes for patients with lymphangioleiomyomatosis in a national clinical centre

artículo científico publicado en 2015

A theoretical model of inflammation- and mechanotransduction-driven asthmatic airway remodelling

artículo científico publicado en 2018

Accelerated extracellular matrix turnover during exacerbations of COPD.

artículo científico publicado en 2015

Air travel in women with lymphangioleiomyomatosis.

artículo científico publicado en 2006

An assay to evaluate the long term effects of inflammatory mediators on airway smooth muscle: evidence that TNF(alpha)up-regulates 5-HT(2A) mediated contraction

artículo científico publicado en 2002

Analysis of the oestrogen response in an angiomyolipoma derived xenograft model

artículo científico publicado en 2008

Association of MMP-2 polymorphisms with severe and very severe COPD: a case control study of MMPs-1, 9 and 12 in a European population

artículo científico publicado en 2010

CCR3 induced-p42/44 MAPK activation protects against staurosporine induced-DNA fragmentation but not apoptosis in airway smooth muscle cells.

artículo científico publicado en 2012

Cardiovascular and inflammatory effects of simvastatin therapy in patients with COPD: a randomized controlled trial

artículo científico publicado en 2015

Cathepsin K in Lymphangioleiomyomatosis: LAM Cell-Fibroblast Interactions Enhance Protease Activity by Extracellular Acidification.

artículo científico publicado en 2017

Chronic Respiratory Diseases. Rare lung diseases. Introduction

artículo científico publicado en 2005

Clinical experience of lymphangioleiomyomatosis in the UK. ⬇️

artículo científico publicado en 2000

Clinical utility of diagnostic guidelines and putative biomarkers in lymphangioleiomyomatosis.

artículo científico publicado en 2012

Collagen I and thrombin activate MMP-2 by MMP-14-dependent and -independent pathways: implications for airway smooth muscle migration.

artículo científico publicado en 2006

Cross-sectional study of reversible airway obstruction in LAM: better evidence is needed for bronchodilator and inhaled steroid use

artículo científico publicado en 2019

Discoidin domain receptor 1 regulates bronchial epithelial repair and matrix metalloproteinase production

artículo científico publicado en 2010

ECM Crosslinking Enhances Fibroblast Growth and Protects Against Matrix Proteolysis in Lung Fibrosis.

artículo científico publicado en 2017

Effect of doxycycline on proliferation, MMP production, and adhesion in LAM-related cells

artículo científico publicado en 2010

Emerging clinical picture of lymphangioleiomyomatosis.

artículo científico publicado en 2005

Evolution of lung pathology in lymphangioleiomyomatosis: associations with disease course and treatment response

scientific article published on 30 April 2020

Extra-cellular matrix proteins induce matrix metalloproteinase-1 (MMP-1) activity and increase airway smooth muscle contraction in asthma

artículo científico publicado en 2014

Fungal recognition enhances mannose receptor shedding through dectin-1 engagement

artículo científico publicado en 2011

In search of the fibrotic epithelial cell: opportunities for a collaborative network.

artículo científico publicado en 2011

Interstitial lung disease following certolizumab pegol.

artículo científico publicado en 2011

Levels of circulating MMP-7 degraded elastin are elevated in pulmonary disorders.

artículo científico publicado en 2015

Living with lymphangioleiomyomatosis

artículo científico publicado en 2010

Lung function response and side effects to rapamycin for lymphangioleiomyomatosis: a prospective national cohort study

artículo científico publicado en 2017

Lymphangioleiomyomatosis

scientific article published on 01 May 2006

Lymphangioleiomyomatosis

artículo científico publicado en 2016

Lymphangioleiomyomatosis Diagnosis and Management: High-Resolution Chest Computed Tomography, Transbronchial Lung Biopsy, and Pleural Disease Management. An Official American Thoracic Society/Japanese Respiratory Society Clinical Practice Guideline.

artículo científico publicado en 2017

MMP-9 protein level does not reflect overall MMP activity in the airways of patients with COPD.

artículo científico publicado en 2008

Machine learning can predict disease manifestations and outcomes in lymphangioleiomyomatosis

scientific article published on 10 December 2020

Matrix Metalloproteinase-1 Activation Contributes to Airway Smooth Muscle Growth and Asthma Severity.

artículo científico publicado en 2016

Matrix metalloproteinase expression and activity in human airway smooth muscle cells.

artículo científico publicado en 2004

Matrix metalloproteinase-12 (MMP-12) SNP affects MMP activity, lung macrophage infiltration and protects against emphysema in COPD.

artículo científico publicado en 2011

Matrix metalloproteinases -8 and -9 in the Airways, Blood and Urine During Exacerbations of COPD.

artículo científico publicado en 2015

Natural history of angiomyolipoma in lymphangioleiomyomatosis: implications for screening and surveillance

artículo científico publicado en 2014

Official American Thoracic Society/Japanese Respiratory Society Clinical Practice Guidelines: Lymphangioleiomyomatosis Diagnosis and Management

artículo científico publicado en 2016

Perspectives for improving the evaluation and access of therapies for rare lung diseases in Europe

artículo científico publicado en 2012

Pneumothorax and the biology of Birt-Hogg-Dubé syndrome

scientific article published on 01 June 2020

Pregnancy experiences among women with lymphangioleiomyomatosis

artículo científico publicado en 2008

Pregnancy in lymphangioleiomyomatosis: clinical and lung function outcomes in two national cohorts

artículo científico publicado en 2020

Presence of a prothrombotic state in people with idiopathic pulmonary fibrosis: a population-based case-control study.

artículo científico publicado en 2013

Reply to: Treatment of Pulmonary Lymphangioleiomyomatosis During Pregnancy.

artículo científico publicado en 2018

Residual Lung Abnormalities after COVID-19 Hospitalization: Interim Analysis of the UKILD Post–COVID-19 Study

artículo científico publicado en 2023

Role of the CXCR4/CXCL12 axis in lymphangioleiomyomatosis and angiomyolipoma

artículo científico publicado en 2010

Secretory leukocyte protease inhibitor gene deletion alters bleomycin-induced lung injury, but not development of pulmonary fibrosis

artículo científico publicado en 2016

Sirolimus therapy for angiomyolipoma in tuberous sclerosis and sporadic lymphangioleiomyomatosis: a phase 2 trial

artículo científico publicado en 2011

Sirolimus therapy in tuberous sclerosis or sporadic lymphangioleiomyomatosis

artículo científico publicado en 2008

Sphingolipid, fatty acid and phospholipid metabolites are associated with disease severity and mTOR inhibition in lymphangioleiomyomatosis

artículo científico publicado en 2020

Study of breast cancer incidence in patients of lymphangioleiomyomatosis.

artículo científico publicado en 2016

Subcellular distribution of the TSC2 gene product tuberin in human airway smooth muscle cells is driven by multiple localization sequences and is cell-cycle dependent

artículo científico publicado en 2006

Survival and disease progression in UK patients with lymphangioleiomyomatosis.

artículo científico publicado en 2004

Synthetic functions of airway smooth muscle in asthma

artículo científico publicado en 1997

TAILS proteomics reveals dynamic changes in airway proteolysis controlling protease activity and innate immunity during COPD exacerbations

artículo científico publicado en 2018

TIMP-1 in asthma: guilty by association

artículo científico publicado en 2005

The ERS guidelines for LAM: trying a rationale approach to a rare disease

artículo científico publicado en 2010

The International LAM Registry: a component of an innovative web-based clinician, researcher, and patient-driven rare disease research platform.

artículo científico

The TSC-2 product tuberin is expressed in lymphangioleiomyomatosis and angiomyolipoma.

artículo científico publicado en 2002

The UK guidelines for management and surveillance of Tuberous Sclerosis Complex

scientific article published on 01 March 2019

The clinical profile of tuberous sclerosis complex (TSC) in the United Kingdom: A retrospective cohort study in the Clinical Practice Research Datalink (CPRD).

artículo científico publicado en 2015

The economic burden of tuberous sclerosis complex in the UK: A retrospective cohort study in the Clinical Practice Research Datalink

artículo científico publicado en 2016

The role of extracellular matrix quality in pulmonary fibrosis.

artículo científico

The role of inflammation resolution speed in airway smooth muscle mass accumulation in asthma: insight from a theoretical model

artículo científico publicado en 2014

Tissue and matrix influences on airway smooth muscle function

artículo científico publicado en 2008

Untangling the protease web in COPD: metalloproteinases in the silent zone

artículo científico publicado en 2016

Use of a three-dimensional cell culture model to study airway smooth muscle-mast cell interactions in airway remodeling

artículo científico publicado en 2009

Wild type mesenchymal cells contribute to the lung pathology of lymphangioleiomyomatosis

artículo científico publicado en 2015

Lista de obras de Simon R. Johnson

A 2-year randomised placebo-controlled trial of doxycycline for lymphangioleiomyomatosis.

A 4-year prospective evaluation of protocols to improve clinical outcomes for patients with lymphangioleiomyomatosis in a national clinical centre

A theoretical model of inflammation- and mechanotransduction-driven asthmatic airway remodelling

Accelerated extracellular matrix turnover during exacerbations of COPD.

Air travel in women with lymphangioleiomyomatosis.

An assay to evaluate the long term effects of inflammatory mediators on airway smooth muscle: evidence that TNF(alpha)up-regulates 5-HT(2A) mediated contraction

Analysis of the oestrogen response in an angiomyolipoma derived xenograft model

Association of MMP-2 polymorphisms with severe and very severe COPD: a case control study of MMPs-1, 9 and 12 in a European population

CCR3 induced-p42/44 MAPK activation protects against staurosporine induced-DNA fragmentation but not apoptosis in airway smooth muscle cells.

Cardiovascular and inflammatory effects of simvastatin therapy in patients with COPD: a randomized controlled trial

Cathepsin K in Lymphangioleiomyomatosis: LAM Cell-Fibroblast Interactions Enhance Protease Activity by Extracellular Acidification.

Chronic Respiratory Diseases. Rare lung diseases. Introduction

Clinical experience of lymphangioleiomyomatosis in the UK. ⬇️

Clinical utility of diagnostic guidelines and putative biomarkers in lymphangioleiomyomatosis.

Collagen I and thrombin activate MMP-2 by MMP-14-dependent and -independent pathways: implications for airway smooth muscle migration.

Cross-sectional study of reversible airway obstruction in LAM: better evidence is needed for bronchodilator and inhaled steroid use

Discoidin domain receptor 1 regulates bronchial epithelial repair and matrix metalloproteinase production

ECM Crosslinking Enhances Fibroblast Growth and Protects Against Matrix Proteolysis in Lung Fibrosis.

Effect of doxycycline on proliferation, MMP production, and adhesion in LAM-related cells

Emerging clinical picture of lymphangioleiomyomatosis.

Evolution of lung pathology in lymphangioleiomyomatosis: associations with disease course and treatment response

Extra-cellular matrix proteins induce matrix metalloproteinase-1 (MMP-1) activity and increase airway smooth muscle contraction in asthma

Fungal recognition enhances mannose receptor shedding through dectin-1 engagement

In search of the fibrotic epithelial cell: opportunities for a collaborative network.

Interstitial lung disease following certolizumab pegol.

Levels of circulating MMP-7 degraded elastin are elevated in pulmonary disorders.

Living with lymphangioleiomyomatosis

Lung function response and side effects to rapamycin for lymphangioleiomyomatosis: a prospective national cohort study

Lymphangioleiomyomatosis

Lymphangioleiomyomatosis

Lymphangioleiomyomatosis Diagnosis and Management: High-Resolution Chest Computed Tomography, Transbronchial Lung Biopsy, and Pleural Disease Management. An Official American Thoracic Society/Japanese Respiratory Society Clinical Practice Guideline.

MMP-9 protein level does not reflect overall MMP activity in the airways of patients with COPD.

Machine learning can predict disease manifestations and outcomes in lymphangioleiomyomatosis

Matrix Metalloproteinase-1 Activation Contributes to Airway Smooth Muscle Growth and Asthma Severity.

Matrix metalloproteinase expression and activity in human airway smooth muscle cells.

Matrix metalloproteinase-12 (MMP-12) SNP affects MMP activity, lung macrophage infiltration and protects against emphysema in COPD.

Matrix metalloproteinases -8 and -9 in the Airways, Blood and Urine During Exacerbations of COPD.

Natural history of angiomyolipoma in lymphangioleiomyomatosis: implications for screening and surveillance

Official American Thoracic Society/Japanese Respiratory Society Clinical Practice Guidelines: Lymphangioleiomyomatosis Diagnosis and Management

Perspectives for improving the evaluation and access of therapies for rare lung diseases in Europe

Pneumothorax and the biology of Birt-Hogg-Dubé syndrome

Pregnancy experiences among women with lymphangioleiomyomatosis

Pregnancy in lymphangioleiomyomatosis: clinical and lung function outcomes in two national cohorts

Presence of a prothrombotic state in people with idiopathic pulmonary fibrosis: a population-based case-control study.

Reply to: Treatment of Pulmonary Lymphangioleiomyomatosis During Pregnancy.

Residual Lung Abnormalities after COVID-19 Hospitalization: Interim Analysis of the UKILD Post–COVID-19 Study

Role of the CXCR4/CXCL12 axis in lymphangioleiomyomatosis and angiomyolipoma

Secretory leukocyte protease inhibitor gene deletion alters bleomycin-induced lung injury, but not development of pulmonary fibrosis

Sirolimus therapy for angiomyolipoma in tuberous sclerosis and sporadic lymphangioleiomyomatosis: a phase 2 trial

Sirolimus therapy in tuberous sclerosis or sporadic lymphangioleiomyomatosis

Sphingolipid, fatty acid and phospholipid metabolites are associated with disease severity and mTOR inhibition in lymphangioleiomyomatosis

Study of breast cancer incidence in patients of lymphangioleiomyomatosis.

Subcellular distribution of the TSC2 gene product tuberin in human airway smooth muscle cells is driven by multiple localization sequences and is cell-cycle dependent

Survival and disease progression in UK patients with lymphangioleiomyomatosis.

Synthetic functions of airway smooth muscle in asthma

TAILS proteomics reveals dynamic changes in airway proteolysis controlling protease activity and innate immunity during COPD exacerbations

TIMP-1 in asthma: guilty by association

The ERS guidelines for LAM: trying a rationale approach to a rare disease

The International LAM Registry: a component of an innovative web-based clinician, researcher, and patient-driven rare disease research platform.

The TSC-2 product tuberin is expressed in lymphangioleiomyomatosis and angiomyolipoma.

The UK guidelines for management and surveillance of Tuberous Sclerosis Complex

The clinical profile of tuberous sclerosis complex (TSC) in the United Kingdom: A retrospective cohort study in the Clinical Practice Research Datalink (CPRD).

The economic burden of tuberous sclerosis complex in the UK: A retrospective cohort study in the Clinical Practice Research Datalink

The role of extracellular matrix quality in pulmonary fibrosis.

The role of inflammation resolution speed in airway smooth muscle mass accumulation in asthma: insight from a theoretical model

Tissue and matrix influences on airway smooth muscle function

Untangling the protease web in COPD: metalloproteinases in the silent zone

Use of a three-dimensional cell culture model to study airway smooth muscle-mast cell interactions in airway remodeling

Wild type mesenchymal cells contribute to the lung pathology of lymphangioleiomyomatosis